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Vulvar Cancer

Rare Cancer

Category: 婦人科ICD-10: C51

Overview

Vulvar cancer is a malignancy of the external female genitalia, with squamous cell carcinoma accounting for about 90% of cases. It predominantly affects older women, with HPV infection and chronic vulvar conditions (lichen sclerosus) as major risk factors.

Symptoms

Vulvar itching, a lump or nodule, and ulceration are common early symptoms. Advanced disease may present with pain, bleeding, and inguinal lymph node enlargement.

Diagnosis

Visual examination and punch biopsy provide histological diagnosis. CT and MRI evaluate depth of invasion and lymph node metastasis for staging.

Treatments

Early-stage disease is treated with wide local excision and sentinel lymph node biopsy. Advanced cases require inguinofemoral lymph node dissection and adjuvant chemoradiation. Unresectable disease is managed with concurrent cisplatin-based chemoradiation.

Latest Research & Approaches

Immune checkpoint inhibitors are being evaluated in clinical trials for advanced and recurrent vulvar cancer. Therapeutic HPV vaccine approaches for HPV-related vulvar cancer are also under investigation.

Sources & References

NCI - Vulvar Cancer Treatment
American Cancer Society - Vulvar Cancer
NCCN Guidelines: Vulvar Cancer

Hospitals with Treatment Experience

The following hospitals have documented treatment experience for this cancer (based on DPC public data and hospital cancer registry).

Mie University Hospital

三重県 津市

Website

National Cancer Center Hospital

東京都 中央区

Website

Shinshu University Hospital

長野県 松本市

Website

Tohoku University Hospital

宮城県 仙台市

Website

Kumamoto University Hospital

熊本県 熊本市

Website

The Cancer Institute Hospital of JFCR

東京都 江東区

Website

Tokushima University Hospital

徳島県 徳島市

Website

Kagoshima University Hospital

鹿児島県 鹿児島市

Website

Osaka International Cancer Institute

大阪府 大阪市

Website

Kanazawa University Hospital

石川県 金沢市

Website

Source: Ministry of Health, Labour and Welfare DPC Public Data / National Cancer Center Hospital Cancer Registry

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